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The non-compact left ventricle cardiomyopathy: clinical features and diagnostic capabilities

https://doi.org/10.20996/1819-6446-2015-11-6-638-642

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Abstract

The non-compact left ventricular cardiomyopathy (NCLVC) refers to the non-classified cardiomyopathies. Its cause is not completely clear. NCLVC is characterized by an increased trabecular with the formation of deep intertrabecular crypts. It can exist either in isolated form or in combination with other congenital diseases. The clinical features of NCLVC are different: asymptomatic forms are identified as well as forms with the progressive course of the disease, with heart failure, angina, thromboembolic complications, and ventricular arrhythmias. In some cases, the disease starts with the sudden cardiac death. The sudden decompensation of NCLVC also could arise due to the development of acute myocarditis

About the Authors

E. A. Mershina
Treatment and Rehabilitation Center. Ivankovskoe shosse 3, Moscow, 125367 Russia Russian Medical Academy of Postgraduate Education. Barricadnaya ul. 2/1, Moscow, 123995 Russia
Russian Federation


R. P. Myasnikov
State Research Centre for Preventive Medicine. Petroverigsky per. 10, Moscow, 101990 Russia
Russian Federation


O. V. Kulikova
State Research Centre for Preventive Medicine. Petroverigsky per. 10, Moscow, 101990 Russia
Russian Federation


M. S. Kharlap
State Research Centre for Preventive Medicine. Petroverigsky per. 10, Moscow, 101990 Russia
Russian Federation


S. N. Koretskiy
State Research Centre for Preventive Medicine. Petroverigsky per. 10, Moscow, 101990 Russia
Russian Federation


O. M. Larina
Treatment and Rehabilitation Center. Ivankovskoe shosse 3, Moscow, 125367 Russia
Russian Federation


V. E. Sinitsyn
Treatment and Rehabilitation Center. Ivankovskoe shosse 3, Moscow, 125367 Russia Russian Medical Academy of Postgraduate Education. Barricadnaya ul. 2/1, Moscow, 123995 Russia
Russian Federation


S. A. Boytsov
State Research Centre for Preventive Medicine. Petroverigsky per. 10, Moscow, 101990 Russia
Russian Federation


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For citation:


Mershina E.A., Myasnikov R.P., Kulikova O.V., Kharlap M.S., Koretskiy S.N., Larina O.M., Sinitsyn V.E., Boytsov S.A. The non-compact left ventricle cardiomyopathy: clinical features and diagnostic capabilities. Rational Pharmacotherapy in Cardiology. 2015;11(6):638-642. (In Russ.) https://doi.org/10.20996/1819-6446-2015-11-6-638-642

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