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CHRONIC THROMBOEMBOLIC PULMONARY HYPERTENSION AND PROBLEMS OF RARE AND INTERDISCIPLINARY DISEASE

https://doi.org/10.20996/1819-6446-2014-10-1-73-78

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Abstract

Chronic thromboembolic pulmonary hypertension (CTEPH) is a rare life-threatening disease with a prevalence of 2 cases per 100000 population. CTEPH is a chronic, progressive disease characterized by high disability and mortality rates in young and middle-aged people, often with underlying genetic and autoimmune thrombophilic disorders. The need for pathogenetic therapy with orphan drugs that can slow the progression of the disease is supported.

About the Authors

N. A. Shostak
Pirogov Russian National Research Medical University, Moscow
Russian Federation


A. A. Klimenko
Pirogov Russian National Research Medical University, Moscow
Russian Federation


N. A. Demidova
Pirogov Russian National Research Medical University, Moscow
Russian Federation


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For citation:


Shostak N.A., Klimenko A.A., Demidova N.A. CHRONIC THROMBOEMBOLIC PULMONARY HYPERTENSION AND PROBLEMS OF RARE AND INTERDISCIPLINARY DISEASE. Rational Pharmacotherapy in Cardiology. 2014;10(1):73-78. (In Russ.) https://doi.org/10.20996/1819-6446-2014-10-1-73-78

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